 G40 |
 |
Epilepsy and recurrent seizures  |
| |
| Notes |
the following terms are to be considered equivalent to intractable: pharmacoresistant (pharmacologically resistant), treatment resistant, refractory (medically) and poorly controlled
|
| Excludes1 |
conversion disorder with seizures (F44.5)
convulsions NOS (R56.9)
post traumatic seizures (R56.1)
seizure (convulsive) NOS (R56.9)
seizure of newborn (P90)
|
| Excludes2 |
hippocampal sclerosis (G93.81)
mesial temporal sclerosis (G93.81)
temporal sclerosis (G93.81)
Todd's paralysis (G83.84)
|
|
| |
| G40.0 |
|
Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset |
| |
| Benign childhood epilepsy with centrotemporal EEG spikes | | Childhood epilepsy with occipital EEG paroxysms |
| Excludes1 |
adult onset localization-related epilepsy (G40.1-, G40.2-)
|
|
| |
| G40.00 |
|
Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable |
| |
| Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset without intractability |
|
| |
 G40.001 |
|
Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable, with status epilepticus |
| | |
| G40.009 |
|
Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable, without status epilepticus |
| |
| Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset NOS |
|
| | | |
| G40.01 |
|
Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable |
| |
| G40.011 |
|
Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable, with status epilepticus |
| | |
| G40.019 |
|
Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable, without status epilepticus |
| | |
| |
| G40.1 |
|
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures |
| |
| Attacks without alteration of consciousness | | Epilepsia partialis continua [Kozhevnikof] | | Simple partial seizures developing into secondarily generalized seizures |
|
| |
| G40.10 |
|
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable |
| |
| Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures without intractability |
|
| |
| G40.101 |
|
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, with status epilepticus |
| | |
| G40.109 |
|
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, without status epilepticus |
| |
| Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures NOS |
|
| | | |
| G40.11 |
|
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable |
| |
| G40.111 |
|
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, with status epilepticus |
| | |
| G40.119 |
|
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, without status epilepticus |
| | |
| |
| G40.2 |
|
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures |
| |
| Attacks with alteration of consciousness, often with automatisms | | Complex partial seizures developing into secondarily generalized seizures |
|
| |
| G40.20 |
|
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable |
| |
| Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures without intractability |
|
| |
| G40.201 |
|
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable, with status epilepticus |
| | |
| G40.209 |
|
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable, without status epilepticus |
| |
| Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures NOS |
|
| | | |
| G40.21 |
|
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable |
| |
| G40.211 |
|
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable, with status epilepticus |
| | |
| G40.219 |
|
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable, without status epilepticus |
| | |
| |
| G40.3 |
|
Generalized idiopathic epilepsy and epileptic syndromes |
| |
| CodeAlso |
MERRF syndrome, if applicable (E88.42)
|
|
| |
| G40.30 |
|
Generalized idiopathic epilepsy and epileptic syndromes, not intractable |
| |
| Generalized idiopathic epilepsy and epileptic syndromes without intractability |
|
| |
| G40.301 |
|
Generalized idiopathic epilepsy and epileptic syndromes, not intractable, with status epilepticus |
| | |
| G40.309 |
|
Generalized idiopathic epilepsy and epileptic syndromes, not intractable, without status epilepticus |
| |
| Generalized idiopathic epilepsy and epileptic syndromes NOS |
|
| | | |
| G40.31 |
|
Generalized idiopathic epilepsy and epileptic syndromes, intractable |
| |
| G40.311 |
|
Generalized idiopathic epilepsy and epileptic syndromes, intractable, with status epilepticus |
| | |
| G40.319 |
|
Generalized idiopathic epilepsy and epileptic syndromes, intractable, without status epilepticus |
| | |
| |
| G40.A |
|
Absence epileptic syndrome |
| |
| Childhood absence epilepsy [pyknolepsy] | | Juvenile absence epilepsy | | Absence epileptic syndrome, NOS |
|
| |
| G40.A0 |
|
Absence epileptic syndrome, not intractable |
| |
| G40.A01 |
|
Absence epileptic syndrome, not intractable, with status epilepticus |
| | |
| G40.A09 |
|
Absence epileptic syndrome, not intractable, without status epilepticus |
| | | |
| G40.A1 |
|
Absence epileptic syndrome, intractable |
| |
| G40.A11 |
|
Absence epileptic syndrome, intractable, with status epilepticus |
| | |
| G40.A19 |
|
Absence epileptic syndrome, intractable, without status epilepticus |
| | |
| |
| G40.B |
|
Juvenile myoclonic epilepsy [impulsive petit mal] |
| |
| G40.B0 |
|
Juvenile myoclonic epilepsy, not intractable |
| |
| G40.B01 |
|
Juvenile myoclonic epilepsy, not intractable, with status epilepticus |
| | |
| G40.B09 |
|
Juvenile myoclonic epilepsy, not intractable, without status epilepticus |
| | | |
| G40.B1 |
|
Juvenile myoclonic epilepsy, intractable |
| |
| G40.B11 |
|
Juvenile myoclonic epilepsy, intractable, with status epilepticus |
| | |
| G40.B19 |
|
Juvenile myoclonic epilepsy, intractable, without status epilepticus |
| | |
| |
| G40.C |
|
Lafora progressive myoclonus epilepsy |
| |
| Lafora body disease |
| CodeAlso |
, if applicable, associated conditions such as dementia (F02.8-)
|
|
| |
| G40.C0 |
|
Lafora progressive myoclonus epilepsy, not intractable |
| |
| G40.C01 |
|
Lafora progressive myoclonus epilepsy, not intractable, with status epilepticus |
| | |
| G40.C09 |
|
Lafora progressive myoclonus epilepsy, not intractable, without status epilepticus |
| |
| Lafora progressive myoclonus epilepsy NOS |
|
| | | |
| G40.C1 |
|
Lafora progressive myoclonus epilepsy, intractable |
| |
| G40.C11 |
|
Lafora progressive myoclonus epilepsy, intractable, with status epilepticus |
| | |
| G40.C19 |
|
Lafora progressive myoclonus epilepsy, intractable, without status epilepticus |
| | |
| |
| G40.4 |
|
Other generalized epilepsy and epileptic syndromes |
| |
| Epilepsy with grand mal seizures on awakening | | Epilepsy with myoclonic absences | | Epilepsy with myoclonic-astatic seizures | | Grand mal seizure NOS | | Nonspecific atonic epileptic seizures | | Nonspecific clonic epileptic seizures | | Nonspecific myoclonic epileptic seizures | | Nonspecific tonic epileptic seizures | | Nonspecific tonic-clonic epileptic seizures | | Symptomatic early myoclonic encephalopathy |
|
| |
| G40.40 |
|
Other generalized epilepsy and epileptic syndromes, not intractable |
| |
| Other generalized epilepsy and epileptic syndromes without intractability | | Other generalized epilepsy and epileptic syndromes NOS |
|
| |
| G40.401 |
|
Other generalized epilepsy and epileptic syndromes, not intractable, with status epilepticus |
| | |
| G40.409 |
|
Other generalized epilepsy and epileptic syndromes, not intractable, without status epilepticus |
| | | |
| G40.41 |
|
Other generalized epilepsy and epileptic syndromes, intractable |
| |
| G40.411 |
|
Other generalized epilepsy and epileptic syndromes, intractable, with status epilepticus |
| | |
| G40.419 |
|
Other generalized epilepsy and epileptic syndromes, intractable, without status epilepticus |
| | | |
| G40.42 |
|
Cyclin-Dependent Kinase-Like 5 Deficiency Disorder |
| |
| CDKL5 |
| UseAdditionalCode |
code, if known, to identify associated manifestations, such as:
cortical blindness (H47.61-)
global developmental delay (F88)
|
|
| |
| |
| G40.5 |
|
Epileptic seizures related to external causes |
| |
| Epileptic seizures related to alcohol | | Epileptic seizures related to drugs | | Epileptic seizures related to hormonal changes | | Epileptic seizures related to sleep deprivation | | Epileptic seizures related to stress |
| CodeAlso |
, if applicable, associated epilepsy and recurrent seizures (G40.-)
|
| UseAdditionalCode |
code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
|
|
| |
| G40.50 |
|
Epileptic seizures related to external causes, not intractable |
| |
| G40.501 |
|
Epileptic seizures related to external causes, not intractable, with status epilepticus |
| | |
| G40.509 |
|
Epileptic seizures related to external causes, not intractable, without status epilepticus |
| |
| Epileptic seizures related to external causes, NOS |
|
| | |
| |
| G40.8 |
|
Other epilepsy and recurrent seizures |
| |
| Epilepsies and epileptic syndromes undetermined as to whether they are focal or generalized | | Landau-Kleffner syndrome |
|
| |
| G40.80 |
|
Other epilepsy |
| |
| G40.801 |
|
Other epilepsy, not intractable, with status epilepticus |
| |
| Other epilepsy without intractability with status epilepticus |
|
| | |
| G40.802 |
|
Other epilepsy, not intractable, without status epilepticus |
| |
| Other epilepsy NOS | | Other epilepsy without intractability without status epilepticus |
|
| | |
| G40.803 |
|
Other epilepsy, intractable, with status epilepticus |
| | |
| G40.804 |
|
Other epilepsy, intractable, without status epilepticus |
| | | |
| G40.81 |
|
Lennox-Gastaut syndrome |
| |
| G40.811 |
|
Lennox-Gastaut syndrome, not intractable, with status epilepticus |
| | |
| G40.812 |
|
Lennox-Gastaut syndrome, not intractable, without status epilepticus |
| | |
| G40.813 |
|
Lennox-Gastaut syndrome, intractable, with status epilepticus |
| | |
| G40.814 |
|
Lennox-Gastaut syndrome, intractable, without status epilepticus |
| | | |
| G40.82 |
|
Epileptic spasms |
| |
| Infantile spasms | | Salaam attacks | | West's syndrome |
|
| |
| G40.821 |
|
Epileptic spasms, not intractable, with status epilepticus |
| | |
| G40.822 |
|
Epileptic spasms, not intractable, without status epilepticus |
| | |
| G40.823 |
|
Epileptic spasms, intractable, with status epilepticus |
| | |
| G40.824 |
|
Epileptic spasms, intractable, without status epilepticus |
| | | |
| G40.83 |
|
Dravet syndrome |
| |
| Polymorphic epilepsy in infancy (PMEI) | | Severe myoclonic epilepsy in infancy (SMEI) |
|
| |
| G40.833 |
|
Dravet syndrome, intractable, with status epilepticus |
| | |
| G40.834 |
|
Dravet syndrome, intractable, without status epilepticus |
| |
|
| | | |
| G40.84 |
|
KCNQ2-related epilepsy |
| |
| G40.841 |
|
KCNQ2-related epilepsy, not intractable, with status epilepticus |
| | |
| G40.842 |
|
KCNQ2-related epilepsy, not intractable, without status epilepticus |
| |
| KCNQ2-related epilepsy NOS |
|
| | |
| G40.843 |
|
KCNQ2-related epilepsy, intractable, with status epilepticus |
| | |
| G40.844 |
|
KCNQ2-related epilepsy, intractable, without status epilepticus |
| | | |
| G40.89 |
|
Other seizures |
| |
| Excludes1 |
post traumatic seizures (R56.1)
recurrent seizures NOS (G40.909)
seizure NOS (R56.9)
|
|
| |
| |
| G40.9 |
|
Epilepsy, unspecified |
| |
| G40.90 |
|
Epilepsy, unspecified, not intractable |
| |
| Epilepsy, unspecified, without intractability |
|
| |
| G40.901 |
|
Epilepsy, unspecified, not intractable, with status epilepticus |
| | |
| G40.909 |
|
Epilepsy, unspecified, not intractable, without status epilepticus |
| |
| Epilepsy NOS | | Epileptic convulsions NOS | | Epileptic fits NOS | | Epileptic seizures NOS | | Recurrent seizures NOS | | Seizure disorder NOS |
|
| | | |
| G40.91 |
|
Epilepsy, unspecified, intractable |
| |
| Intractable seizure disorder NOS |
|
| |
| G40.911 |
|
Epilepsy, unspecified, intractable, with status epilepticus |
| | |
| G40.919 |
|
Epilepsy, unspecified, intractable, without status epilepticus |
| | |