D47 | 
		 | 
		Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue   | 
	
 |  | 
	
		 D47.0 | 
		  | 
		Mast cell neoplasms of uncertain behavior | 
	 
	
		 |  | 
		
	
		| Excludes1 | 
		congenital cutaneous mastocytosis (Q82.2) histiocytic neoplasms of uncertain behavior (D47.Z9) malignant mast cell neoplasm (C96.2-)
  | 
	 
 
 | 
	  |  | 
	
		 D47.01 | 
		  | 
		Cutaneous mastocytosis | 
	 
	
		 |  | 
		
| Diffuse cutaneous mastocytosis |  | Maculopapular cutaneous mastocytosis |  | Solitary mastocytoma |  | Telangiectasia macularis eruptiva perstans |  | Urticaria pigmentosa |  	
		| Excludes1 | 
		congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2) congenital urticaria pigmentosa (Q82.2) extracutaneous mastocytoma (D47.09)
  | 
	 
 
 | 
	   |   |  | 
	
		 D47.02 | 
		  | 
		Systemic mastocytosis | 
	 
	
		 |  | 
		
| Indolent systemic mastocytosis |  | Isolated bone marrow mastocytosis |  | Smoldering systemic mastocytosis |  | Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD) |  	
		| CodeAlso | 
		, if applicable, any associated hematological non-mast cell lineage disease, such as: acute myeloid leukemia (C92.6-, C92.A-) chronic myelomonocytic leukemia (C93.1-) essential thrombocytosis (D47.3) hypereosinophilic syndrome (D72.1) myelodysplastic syndrome (D46.9) myeloproliferative syndrome (D47.1) non-Hodgkin lymphoma (C82-C85) plasma cell myeloma (C90.0-) polycythemia vera (D45)
  | 
	 
	
		| Excludes1 | 
		aggressive systemic mastocytosis (C96.21) mast cell leukemia (C94.3-)
  | 
	 
 
 | 
	   |   |  | 
	
		 D47.09 | 
		  | 
		Other mast cell neoplasms of uncertain behavior | 
	 
	
		 |  | 
		
| Extracutaneous mastocytoma |  | Mast cell tumor NOS |  | Mastocytoma NOS |  | Mastocytosis NOS |   
 | 
	   |    | 
 |  | 
	
		 D47.1 | 
		  | 
		Chronic myeloproliferative disease | 
	 
	
		 |  | 
		
| Chronic neutrophilic leukemia |  | Myeloproliferative disease, unspecified |  	
		| Excludes1 | 
		atypical chronic myeloid leukemia BCR/ABL-negative (C92.2-) chronic myeloid leukemia BCR/ABL-positive (C92.1-) myelofibrosis NOS (D75.81) myelophthisic anemia (D61.82) myelophthisis (D61.82) secondary myelofibrosis NOS (D75.81)
  | 
	 
 
 | 
	   | 
 |  | 
	
		 D47.2 | 
		  | 
		Monoclonal gammopathy | 
	 
	
		 |  | 
		
| Monoclonal gammopathy of undetermined significance [MGUS] |   
 | 
	   | 
 |  | 
	
		 D47.3 | 
		  | 
		Essential (hemorrhagic) thrombocythemia | 
	 
	
		 |  | 
		
| Essential thrombocytosis |  | Idiopathic hemorrhagic thrombocythemia |  | Primary thrombocytosis |  	
		| Excludes2 | 
		reactive thrombocytosis (D75.838) secondary thrombocytosis (D75.838) thrombocythemia NOS (D75.839) thrombocytosis NOS (D75.839)
  | 
	 
 
 | 
	   | 
 |  | 
	
		 D47.4 | 
		  | 
		Osteomyelofibrosis | 
	 
	
		 |  | 
		
| Chronic idiopathic myelofibrosis |  | Myelofibrosis (idiopathic) (with myeloid metaplasia) |  | Myelosclerosis (megakaryocytic) with myeloid metaplasia |  | Secondary myelofibrosis in myeloproliferative disease |  	
		| Excludes1 | 
		acute myelofibrosis (C94.4-)
  | 
	 
 
 | 
	   | 
 |  | 
	
		 D47.Z | 
		 | 
		Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue | 
	 
 |  | 
	
		 D47.Z1 | 
		  | 
		Post-transplant lymphoproliferative disorder (PTLD) | 
	 
	
		 |  | 
		
	
		| CodeFirst | 
		complications of transplanted organs and tissue (T86.-)
  | 
	 
	
		| nonPrimary | 
		Yes
  | 
	 
 
 | 
	   |   |  | 
	
		 D47.Z2 | 
		  | 
		Castleman disease | 
	 
	
		 |  | 
		
	
		| CodeAlso | 
		, if applicable, human herpesvirus 8 infection (B10.89)
  | 
	 
	
		| Excludes2 | 
		Kaposi's sarcoma (C46.-)
  | 
	 
 
 | 
	   |   |  | 
	
		 D47.Z9 | 
		  | 
		Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue | 
	 
	
		 |  | 
		
| Histiocytic tumors of uncertain behavior |   
 | 
	   |    | 
 |  | 
	
		 D47.9 | 
		  | 
		Neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecified | 
	 
	
		 |  | 
		
| Lymphoproliferative disease NOS |   
 | 
	   |